Introduction:
Caseous mitral annulus calcification (CMAC) is an extremely rare condition with controversial etiopathogeny and few clinical symptoms occurring mainly in old women (1). Its diagnosis on echocardiography may be confusing on echocardiography. Computed tomography (CT) is the key diagnostic imaging technique. We here report the case of a 54-year-old women diagnosed with a mitral tumor on echocardiography. The diagnosis was doubtful on cardiac magnetic resonance (CMR). CT concluded to CMAC.