Introduction
A 68-year-old woman with a history of hepatic hydatidectomy two years ago complained of a large right-sided cervical mass. In ultrasound imaging, a huge (45mm×75mm) mass was detected in the base of the right side of the neck. Moreover, multiple cystic lesions involving the two lobes of the liver were found. Despite the absence of cardiac symptoms, transthoracic echocardiographic examination revealed a large (33mm×42 mm) echo lucent cystic mass plugged into the interventricular septum. A positive serology test confirmed the diagnosis of hydatidosis. Treatment with antiprotozoal medication was started, and after two weeks, the patient successfully underwent surgical hydatidectomy using the cardiopulmonary bypass. This case highlights the rare concomitant cardiac, cervical, and hepatic involvement with hydatid disease. Together, a good understanding of the atypical manifestations, potential associated risk factors, and epidemiology leads to the optimal and timely management of such patients to minimize worse outcomes.