Erdheim-Chester disease: a multisystem disease case illustration with
rare manifestations and treatment challenges.
Erdheim-Chester disease is a rare multisystemic disease. A 50-year-old
woman, presented with a recurrent pain and swelling of the left knee.
Bone scintigraphy showed increased tracer uptake of peripheral skeleton.
The computed tomography showed tissular infiltration in the
retroperitoneum, around the vessels. Immunohistochemistry showed CD68
(+) and CD1a (-).