Major Criteria Minor Criteria
Hypomelanotic macules Confetti skin lesion
Angiofibroma Dental enamel pits
Ungual fibroma Intraoral fibromas
Shagreen patch Retinal achromic patch
Multiple retinal hamartomas Multiple renal cysts
Multiple cortical tubers and/ or radial migration lines Non renal hamartomas
Subependymal nodules Sclerotic bone lesion
Subependymal giant cell astrocytoma
Cardiac rhabdomyoma
Lymphangiomyomatosis
Angiomyolipomas