Introduction
Systemic lupus erythematosus (SLE) is an autoimmune disease with multi-organ involvement and is associated with the presence of autoantibodies. Patients with SLE often develop aortic events such as aortic aneurysms and dissections1, 2. Pseudoaneurysms are rare complications after aortic surgery and have been reported in patients with SLE3. However, little is known about true aneurysms of the residual ascending aorta after aortic surgery. We report the case of a patient with SLE who developed a true aneurysm of the ascending aorta 17 years after total arch replacement for an acute aortic dissection.