Introduction:
Mucormycosis is a disease caused by fungi of the order Mucoraceae of the class Zygomycetes. It is a potentially fatal fungal infection that usually affects immunocompromised hosts almost uniformly. Clinically, the rhino-orbito-cerebral location is the most common. Mucormycosis of the external and middle ear is a rare entity. The aim of this case is to illustrate the pathogenesis of this clinical entity, its clinical presentation and diagnosis and to discuss its therapeutic modalities and prognosis.