Introduction
Absent pulmonary valve syndrome (APVS) is a rare congenital cardiac
malformation that has absent, dysplastic, or rudimentary pulmonary valve
leaflets. The characteristic feature of APVS is dilation of the
pulmonary artery, which leads to compression of the tracheobronchial
tree and respiratory distress. Most cases of APVS are associated with
tetralogy of Fallot (ToF). L-transposition of the great arteries (L-TGA)
is also a rare congenital anomaly that is associated with ventricular
septal defect, pulmonary stenosis, and abnormalities of the tricuspid
valve. There are no previous reports on patients with both APVS and
L-TGA.