Introduction
Absent pulmonary valve syndrome (APVS) is a rare congenital cardiac malformation that has absent, dysplastic, or rudimentary pulmonary valve leaflets. The characteristic feature of APVS is dilation of the pulmonary artery, which leads to compression of the tracheobronchial tree and respiratory distress. Most cases of APVS are associated with tetralogy of Fallot (ToF). L-transposition of the great arteries (L-TGA) is also a rare congenital anomaly that is associated with ventricular septal defect, pulmonary stenosis, and abnormalities of the tricuspid valve. There are no previous reports on patients with both APVS and L-TGA.