All Patients (N=245) All Patients (N=245) All Patients (N=245) All Patients (N=245) All Patients (N=245)
Patient characteristics Not followed by cardiac specialist (n=67) Not followed by cardiac specialist (n=67) Followed by cardiac specialist (n=178) Followed by cardiac specialist (n=178) P value
N %, [SD] N %, [SD]
Age at presentation, mean 56 [18.4] 54.8 [14.4] 0.21
Male 48 [19.6] 123 [50.2] 0.76
Race 0.80
White 51 76.1% 142 79.8%
African American 9 13.4% 19 10.7%
Other 7 10.4% 17 9.6%
Follow-up at institution (yrs) 2.24 [2.3] 3.98 [2.1] <.0001
Studies
BAV previously known 14 20.9% 72 40.4% 0.006
Follow-up echocardiogram 23 34.3% 140 78.7% < .001
Follow-up CT or cMRI 2 3.0% 73 41.0% < .001
Comorbidities
Hypertension 40 59.7% 98 55.1% 0.41
Coronary artery disease 10 14.9% 36 20.2% 0.36
BMI, mean (SD) 28.2 [7.3] 29.3 [6.7] 0.2
Family history of heart disease 21 31.3% 79 44.4% 0.038
Conditions at initial presentation
Aortic stenosis or regurgitation (mod-severe) 24 35.8% 80 44.9% 0.24
Ascending aorta (diameter, cm) mean 3.71 [0.7] 3.94 [0.7] 0.039
Aortic root (diameter, cm) mean 3.41 [0.7] 3.45 [0.6] 0.42
Aortic root ≥ 3.5cm 23 34.3% 78 43.8% 0.22
Ejection Fraction at initial echo, mean 58.2 [10.6] 57.7 [11.5] 0.74
Underwent surgery (valve, root, and/or ascending aorta) 3 4.5% 68 39.3% < .001
Overall mortality 16 23.9% 12 6.7% < .001