Δ BMI Δ FEV1 predicted Δ Sweat chloride Δ Sermet score Δ IBMX/ Forskolin
Ivacaftor -0.012 (0.94) 0.008 (0.96) 0.334 (0.02) -0.004 (0.98) -0.059 (0.71)
Lumacaftor 0.143 (0.33) 0.077 (0.60) 0.169 (0.25) 0.066 (0.67) 0.127 (0.42)
Luma/Iva 0.003 (0.98) 0.166 (0.25) -0.001 (0.92) 0.279 (0.06) 0.077 (0.62)