Median (IQR) Range
Ivacaftor [µg/ml] 0.5 (0.3 - 0.8) 0.1 - 9.0
Lumacaftor [µg/ml] 23.5 (17.9 - 33.3) 0.0 - 52.2
Lumacaftor/Ivacaftor 50.8 (35.8 - 82.0) 0 – 390