References:
1. Poli P, Conforti C, Gennari E, Padoan R. Transitory pancreatic
insufficiency in cystic fibrosis children. J Cyst Fibros
2020;19(1):e5–e6.
2. Boon M, Calvo-Lerma J, Claes I, Havermans T, Asseiceira I, Bulfamante
A, Garriga M, Masip E, van Schijndel BAM, Fornes V, et al. Use of a
mobile application for self-management of pancreatic enzyme replacement
therapy is associated with improved gastro-intestinal related quality of
life in children with Cystic Fibrosis. J Cyst Fibros
2020;19(4):562–568.
3. Calvo-Lerma J, Boon M, Colombo C, de Koning B, Asseiceira I, Garriga
M, Roca M, Claes I, Bulfamante A, Walet S, et al. Clinical evaluation of
an evidence-based method based on food characteristics to adjust
pancreatic enzyme supplements dose in cystic fibrosis. J Cyst Fibros
2020;S1569-1993(20)30926-7.
4. Viola G, Mietto L, Secchi F, Ping L, Bruni A. Absorption and
distribution of arachidonate in rats receiving lysophospholipids by oral
route. J Lipid Res 1993;34(11):1843–52.
5. Stallings VA, Tindall AM, Mascarenhas MR, Maqbool A, Schall JI.
Improved residual fat malabsorption and growth in children with cystic
fibrosis treated with a novel oral structured lipid supplement: A
randomized controlled trial. PLoS One 2020;15(5):1–13.
6. Tham A, Katz TE, Sutherland RE, Garg M, Liu V, Tong CW, Brunner R,
Quintano J, Collins C, Ooi CY. Micronutrient intake in children with
cystic fibrosis in Sydney, Australia. J Cyst Fibros 2020;19(1):146–152.
7. Harindhanavudhi T, Wang Q, Dunitz J, Moran A, Moheet A. Prevalence
and factors associated with overweight and obesity in adults with cystic
fibrosis: A single-center analysis. J Cyst Fibros 2020;19(1):139–145.
8. Lahiri T, Sullivan JS, Sartorelli KH, Murphy JJ. Delayed Presentation
of Meconium Ileus in an Infant With Cystic Fibrosis. Pediatrics
2020;146(4).
9. Christensen C, Sivapatham G, McKinney ML, Stammers D.
Sulfhemoglobinemia associated with meconium ileus in cystic fibrosis.
Pediatr Pulmonol 2020;55(10):2496–2497.
10. Morales Morales CA, Gonzalez-Urquijo M, Morales Flores LF,
Quevedo-Fernandez E, Guzmán Huerta EA, Virgilio Hernández-Torre MM.
Proximal intestinal obstruction syndrome (PIOS) in a patient with cystic
fibrosis: A case report. Ann Med Surg 2020;60(December):669–672.
11. Klouda TM, Lindholm E, Poletto E, Rani S, Varlotta L, Velasco J.
Presentation of an H-type tracheoesophageal fistula in an adolescent
male with cystic fibrosis: A case report and review of literature. Clin
Imaging 2020;60(1):38–47.
12. Kuczynski J, Liu Z, Lozupone C, Mcdonald D, Fierer N, Knight R. To
Detect Biologically Relevant Patterns. Nat Methodsat Methods
2010;7(10):813–819.
13. Lozupone CA, Knight R. Species divergence and the measurement of
microbial diversity. FEMS Microbiol Rev 2008;32(4):557–578.
14. Kristensen M, Prevaes SMPJ, Kalkman G, Tramper-Stranders GA, Hasrat
R, de Winter- de Groot KM, Janssens HM, Tiddens HA, van Westreenen M,
Sanders EAM, et al. Development of the gut microbiota in early life: The
impact of cystic fibrosis and antibiotic treatment. J Cyst Fibros
2020;19(4):553–561.
15. Khalaf RT, Furura GT, Wagner BD, Roberson CE, Andrews R, Stevens MJ,
Fillon SA, Zemanick ET HJ. Influence of acid blockade on the
aerodigestive tract microbiome in children with cystic fibrosis. J
Pediatr Gastroenterol Nutr 2021;72(4):520-527.
16. Loman BR, Shrestha CL, Thompson R, Groner JA, Mejias A, Ruoff KL,
O’Toole GA, Bailey MT, Kopp BT. Age and environmental exposures
influence the fecal bacteriome of young children with cystic fibrosis.
Pediatr Pulmonol 2020;55(7):1661–1670.
17. Hayden HS, Eng A, Pope CE, Brittnacher MJ, Vo AT, Weiss EJ, Hager
KR, Martin BD, Leung DH, Heltshe SL, et al. Fecal dysbiosis in infants
with cystic fibrosis is associated with early linear growth failure. Nat
Med 2020;26(2):215–221.
18. Coffey MJ, Low I, Stelzer-Braid S, Wemheuer B, Garg M, Thomas T,
Jaffe A, Rawlinson WD, Ooi CY. The intestinal virome in children with
cystic fibrosis differs from healthy controls. PLoS One
2020;15(5):1–18.
19. Beaufils F, Mas E, Mittaine M, Addra M, Fayon M, Delhaes L, Clouzeau
H, Galode F, Lamireau T. Increased Fecal Calprotectin Is Associated with
Worse Gastrointestinal Symptoms and Quality of Life Scores in Children
with Cystic Fibrosis. 2020:1–14.
20. Siegel MJ, Freeman AJ, Ye W, Palermo JJ, Molleston JP, Paranjape SM,
Stoll J, Leung DH, Masand P, Karmazyn B, et al. Heterogeneous Liver on
Research Ultrasound Identifies Children with Cystic Fibrosis at High
Risk of Advanced Liver Disease: Interim Results of a Prospective
Observational Case-Controlled Study. J Pediatr 2020;219:62-69.e4.
21. Karnsakul W, Wasuwanich P, Ingviya T, Vasilescu A, Carson KA,
Mogayzel PJ, Schwarz KB. A longitudinal assessment of non-invasive
biomarkers to diagnose and predict cystic fibrosis-associated liver
disease. J Cyst Fibros 2020;19(4):546–552.
22. Calvopina DA, Noble C, Weis A, Hartel GF, Ramm LE, Balouch F,
Fernandez-Rojo MA, Coleman MA, Lewindon PJ, Ramm GA. Supersonic
shear-wave elastography and APRI for the detection and staging of liver
disease in pediatric cystic fibrosis. J Cyst Fibros 2020;19(3):449–454.
23. Debray D, Kelly D, Houwen R, Strandvik B, Colombo C. Best practice
guidance for the diagnosis and management of cystic fibrosis-associated
liver disease. J Cyst Fibros 2011;10(SUPPL. 2):S29–S36.