Introduction
Pancreatic cysts are broadly categorized as neoplastic intraductal papillary mucinous neoplasm (IPMN), mucinous cystic neoplasm (MCN), serous cystic neoplasm (SCN), and non-neoplastic (pancreatic pseudocysts, lymphoepithelial cysts, epidermoid cysts, and dermoid cysts). In addition, there are pancreatic neuroendocrine tumors (pNET), in which the tumor has degenerated into cysts. International clinical practice guidelines for pancreatic cystic tumors include the International Association of Pancreatology (IAP) guidelines,1 European expert consensus statements,2 and the American Gastroenterological Association (AGA) guidelines.3 However, there are no guidelines for pancreatic pseudocysts and no clear diagnostic criteria have been established. Pancreatic lymphoepithelial cysts (LECs) are rare benign lesions and were initially described by Luchtrath and Schriefers in 1985.4 In 1987, Truong proposed to call it a lymphoepithelial cyst.5 The cysts are typically observed in middle-aged and elderly men; they occur equally in the pancreatic head, body, or tail, and may present as a single or multilocular lesion. This study presents the case of a patient with a LEC in the pancreatic accessory spleen. This is the first such instance being documented. We believe that our report is valuable as it is the first of its kind on LEC in the pancreatic accessory spleen. Furthermore, the exposure and knowledge acquired through it will enable the development of international diagnostic criteria for LECs and similar epidermoid cysts and dermoid cysts in the future.