Abstract
Angioma serpiginosum is a rare benign nevoid disorder affecting the small vessels of the upper dermis. We are presenting a case of this rare disease in an 11-year-old girl who presented with multiple progressive asymptomatic scattered and confluent punctate erythematous to violaceous macules over the left side of the abdomen in T8-T10 dermatomal distribution with normal surrounding and intervening skin since birth. Histopathological examination (HPE) revealed few ectatic congested thin-walled blood vessels in papillary dermis with few areas of downward growth of the rete ridges between these blood vessels. Based on the clinical and the HPE, a diagnosis of angioma serpiginosum was made. This rare vascular anomaly and abdomen involvement with zosteriform distribution is rarely reported in the literature.