Comparison of qualitative clinical, laboratory and therapeutic variables
between IEI+ and
Abbreviations: DTP, Diphtheria-Tetanus-Pertussis; IEI, Inborn
errors of immunity; IVIG, intravenous immunoglobulins; MMR,
Measles-Mumps-Rubella; obs, observations. Legend: ↓, decrease; ↑,
increase.† Familial immune-mediated disorders (endocrinological,
gastrointestinal, hematological, mucocutaneous, pulmonary and
rheumatological).‡ Invasive infections (bronchopneumonia, cutaneous abscesses,
osteomyelitis, diffuse and/or profound herpetic lesions).§ Recurrent/relapsing infections (recurrent urinary and
respiratory tract infections, mycosis/parasitosis relapsing at least one
time). ¶ Mucocutaneous disorders (alopecia, aphthosis, dermatitis,
granulomas, melanocytic nevi, rosacea, urticarial vasculitis and
warts).†† Pulmonary disorders (asthma, bronchiectasis,
granulomatous-lymphocytic interstitial lung disease, other
interstitiopathies).‡‡ Allergies (asthma, dermatitis, drug and food
allergies/intolerances, rhinoconjunctivitis, Vernal
keratoconjunctivitis).§§Antibody responses to MMR and DTP vaccination detected
respectively through chemiluminescent (microparticle) immunoassay and
enzyme immunoassay.