SUMMARY
Bleeding and clotting in patients with vascular anomalies can come with significant morbidity and mortality. Therefore, it is essential to have an experienced multidisciplinary team which includes a hematologist well-versed in management of coagulopathy in patients with vascular anomalies. Most recommendations are based on small studies, case series and institutional experience. As the field grows and advances, larger prospective studies are needed to identify those patients who are at risk of coagulopathy and establish evidence-based guidelines for evaluation and treatment.