Introduction:
Lipoblastoma is a rare benign neoplasm of the foetal embryonal white fatty tissue occurring most commonly in infants and young children. It frequently occurs in the subcutaneous tissues of the extremities and the trunk[1]. It can also arise in the abdomen, chest, mediastinum, retroperitoneum, and so on. Primary cardiac lipoblastomas are very rare tumours, and involvement of the pulmonary valve is extremely rare. To our knowledge, this is the first report of such a localization of this type of tumour[2,3].