Patient
Current Age (years)
Ivacaftor Initiation
Age of Initiation (years)
Ivacaftor Duration (years)
Initial FE Result (ug/g)*^
Repeat FE Result (ug/g)¥ Repeat FE Result (ug/g) ¥ Repeat FE Result 2023 (ug/g)^Δ
A 4.5 8/2019 1.1 3.4 <15 392
B 5.0 6/2019 1.1 3.9 57 >800
C 5.7 3/2018 0.5 5.2 95 453
D 2.3 7/2021 0.4 1.9 58 >800
E 5.4 2/2019 1.1 4.3 212 <15 21
F 8.3 3/2017 2 6.3 <50 98
G 3.3 8/2020 0.5 2.8 151 375
H 4.0 1/2020 0.6 3.4 43 >500
I 5.6 4/2019 1.4 4.2 485 488 243 606