Univariate analysis Hazard ratio (95% CI)
p
Age Female sex 1.00 (0.97-1.04) 0.95 (0.40-2.27) 0.88 0.92
Diagnosis GPA MPA 1 1.83 (0.42-7.96)
0.42
ANCA pattern Monophasic Remitting Persistent Recurrent 1 1.93 (0.32-11.59) 3.45 (0.63-18.87) 4.26 (0.95-19.07) 0.47 0.15 0.06
Clinical features Constitutional symptoms Fever Anemia Microhaematuria Alveolar haemorrhage Pulmonary infiltrates Pulmonary nodules Mononeuritis multiplex ENT involvement Purpura Arthritis Ocular involvement 0.33 (0.14-0.78) 0.33 (0.13-0.86) 1.34 (0.18-10.05) 1.88 (0.44-8.07) 1.18 (0.48-2.94) 0.85 (0.20-3.72) 1.52 (0.20-11.51) 0.04 (0.00-8.13) 0.28 (0.04-2.12) 0.87 (0.11-6.67) 0.25 (0.08-0.76) 1.07 (0.25-4.62) 0.01 0.02 0.78 0.40 0.71 0.83 0.69 0.23 0.22 0.89 0.01 0.93
Treatment Cyclophosphamide Azathioprine Methotrexate Mycophenolic acid Plasmapheresis Rituximab 0.38 (0.10-1.47) 0.54 (0.21-1.41) 0.04 (0.00-141.05) 0.83 (0.30-2.29) 1.76 (0.50-6.24) 2.18 (0.86-5.52) 0.16 0.21 0.45 0.71 0.38 0.10