C1-INH-HAE Population Type I C1-INH-HAE Type II C1-INH-HAE
Mean age (SD) 33.2 (2.4) 32 (2.6) 39.8 (5.1)
Mean age of symptom’s onset (SD) 12.3 (1.2) 12.6 (1.4) 11.2 (1.5)
Mean age at diagnosis (SD) 30.7 (2.4) 29.2 (2.6) 38.6 (5.2)
Median of diagnostic delay (IQ25-IQ75) 19.3 (2.4) 12.5 (2.3) 25.5 (5.1)
Median of antigenic C1-INH, g/l (SD) 0.06 (0.17) 0.06 (0.03) 0.44 (0.13)
Median of antigenic C4, g/l (SD) 0.08 (0.07) 0.08 (0.07) 0.055 (0.06)
Median of functional C1-INH, % (SD) <15.6 (8.22) <15.6 (8.68) <15.6 (7.57)