Mean age (SD) |
33.2 (2.4) |
32 (2.6) |
39.8
(5.1) |
Mean age of symptom’s onset (SD) |
12.3 (1.2) |
12.6 (1.4) |
11.2 (1.5) |
Mean age at diagnosis (SD) |
30.7 (2.4) |
29.2 (2.6) |
38.6
(5.2) |
Median of diagnostic delay
(IQ25-IQ75) |
19.3 (2.4) |
12.5 (2.3) |
25.5 (5.1) |
Median of antigenic C1-INH, g/l (SD) |
0.06 (0.17) |
0.06
(0.03) |
0.44 (0.13) |
Median of antigenic C4, g/l (SD) |
0.08 (0.07) |
0.08 (0.07) |
0.055 (0.06) |
Median of functional C1-INH, % (SD) |
<15.6 (8.22) |
<15.6 (8.68) |
<15.6 (7.57) |