SURGICAL PATIENTS
Five patients underwent surgical intervention with a median age at
surgery of 20 years (range 10-22). The median diameters at the time of
surgery by echocardiography at the SoV was 47 mm (median Z-score: 7.2),
and at the AAo was 36 mm (median Z-score: 6.4). Three out of the five
patients underwent valve sparing aortic root surgery, one had aortic
valve and root replacement, and one patient underwent Ross procedure.
The two patients with MFS with aortic root dilation underwent valve
sparing aortic root replacement. Three patients had BAV with aortic root
dilation and AI. One patient with BAV underwent valve sparing aortic
root replacement, one underwent Ross procedure, and the last patient had
aortic valve and root replacement.