Introduction
Cardiac rhabdomyoma is the most common primary heart tumor detected in infancy and childhood. The clinical course is generally benign. In studies conducted, spontaneous regression was observed in the majority of cases. The relationship of this tumor, which was first described in 1862, with tuberous sclerosis has been revealed as a result of researches1. Although it has a good clinical course, surgical resection is inevitable when it causes conditions such as ventricular outflow tract obstruction, myocardial dysfunction and malign arrhythmia.2.
Despite many studies, very few congenital heart diseases have been reported in relation to cardiac rhabdomiomas. There are studies that argue that rhabdomyoma can cause any defect by causing a disruption in the embryological development steps of the heart. However, it is still controversial whether these two cardiac pathologies emerge as different pathologies 3 .
We report a rare case of tuberous sclerosis (TS) with cerebral and renal lesions, associated with cardiac rhabdomyoma and atrioventricular septal defect (AVSD).